hemophilia
Množina: hemophilias
(Alternate spelling: haemophilia)
Congenital tendency to uncontrolled bleeding; usually affects males and is transmitted from mother to son; SYN. haemophilia, bleeder's disease.
Any of several inherited diseases in which normal blood clotting is impaired. The sufferer experiences prolonged bleeding from the slightest wound, as well as painful internal bleeding without apparent cause.
Hemophilias are nearly always sex-linked, transmitted through the female line only to male infants; it has afflicted a number of European royal households. Males affected by the most common form are unable to synthesize Factor VIII, a protein involved in the clotting of blood. Treatment is primarily with Factor VIII (now mass-produced from donated blood), but the hemophiliac remains at risk from the slightest incident of bleeding. The disease is a painful one that causes deformities of joints.
An artificial form of factor VIII went on sale 1993 in Germany and Sweden, and in the UK 1994.
Condition marked by uncontrollable bleeding from smallest cuts.
bleeder's disease · haemophilia
hemophilia
hemofilija
IPA: / xemofilija /Sklonost krvavljenju, bolest teškog zaustavljanja krvi (teška porodična i nasledna bolest, koju prenose žene a od koje boluju poglavito muškarci).
Hemofilija je nasledno oboljenje. Ispoljava se sklonošću ka krvavljenju iz nosa, usta, creva i drugih organa, usled nedostatka jednog od činilaca nepohodnih za normalno zaustavljanje krvarenja, odnosno zgrušavanje krvi. Javlja se kod muškaraca. Zaustavlja se samo uz pomoć lekara.
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